Issue N# 3 - 2011
Melanotic neuroectodermal tumor of infancy: Case report and review of the literature
Authors : Camuzard O, Rosello O, Maschi C, Castillo L, Deville A, Boyer C, Chevallier A, Bailleux S. (Nice)
Ref. : Rev Laryngol Otol Rhinol. 2011;132,3:173-176.
Article published in english
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Melanotic Neuroectodermal Tumor of Infancy (MNTI) is a rare but distinct neoplastic entity in infancy. Diagnosis is usually made before the age of 12 months. The common clinical presentation is a rapidly growing mass of the pre-maxillary area. Its surface is unevenly pigmented. To affirm the diagnosis a biopsy is necessary. Few cases of malignancy have been described (5% of cases). Adequate surgical excision is the treatment of choice. Recurrence rate is about 10 to 15% within 5 years. We report in this article the case of a newborn with MNTI illustrating that an R0 surgical excision can be correlated to a favourable prognosis. In this case the 5 years follow up didnít show any local or distant recurrence.
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